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Eosinofil granulomatose med polyangiitt (Churg-Strauss syndrom)

Eosinofil granulomatose med polyangiitt, tidligere kalt Churg-Strauss syndrom, er en sjelden sykdom som nesten utelukkende oppstår hos personer med astma. Årsaken er ukjent.

De første symptomene på Churg-Strauss syndrom er ofte uspesifikke, for eksempel langvarig hoste, snue og bihulebetennelse.

Sist oppdatert:

12. jan. 2022

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Dette dokumentet er basert på det profesjonelle dokumentet Eosinofil granulomatose med polyangiitt (Churg-Strauss) . Referanselisten for dette dokumentet vises nedenfor

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  3. Sinico RA, Bottero P. Churg-Strauss angiitis. Best Pract Res Clin Rheumatol 2009; 23:355. PubMed
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  10. Cottin V, Bel E, Bottero P, et al. Revisiting the systemic vasculitis in eosinophilic granulomatosis with polyangiitis (Churg-Strauss): A study of 157 patients by the Groupe d'Etudes et de Recherche sur les Maladies Orphelines Pulmonaires and the European Respiratory Society Taskforce on eosinophilic granulomatosis with polyangiitis (Churg-Strauss). Autoimmun Rev 2017; 16:1. PubMed
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  12. Bel EH, Wenzel SE, Thompson PJ, et al. Oral Glucocorticoid-Sparing Effect of Mepolizumab in Eosinophilic Asthma. N Engl J Med 2014; 371: 1189-97. doi:10.1056/NEJMoa1403291 DOI
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